Target

Gene symbol :  
Slc25a15
NCBI gene ID :  
18408
Gene full name :  
Solute carrier family 25 member 15
Synonym :  
Ornt1, D630044L02Rik

Protein function

Protein name :  
ORNT1
Mitochondrial ornithine transporter; essential for urea cycle function.

Expected phenotype

Hyperammonemia, growth retardation.

Human disease relevance

Mutations cause hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome.

Model applications

Metabolic disorder models, urea cycle studies.

Keywords:

Mitochondrial transport, Urea cycle, Metabolism

Availability & Delivery:

  • Cryo-recovery using in-house SOPF facilities
  • WoldWide delivery by professional breeders

Slc25a15

conditional Knockout mouse

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hPD-1
hLAG3

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hPD-1
hLAG3

Lorem ipsum dolor sit amet, consectetur adipiscing elit, sed do eiusmod tempor incididunt ut labore et dolore magna aliqua. Ut enim ad minim veniam, quis nostrud exercitation ullamco laboris nisi ut aliquip ex ea commodo consequat. Duis aute irure dolor in reprehenderit in voluptate velit esse cillum dolore eu fugiat nulla pariatur.

hPD-1
hLAG3

Lorem ipsum dolor sit amet, consectetur adipiscing elit, sed do eiusmod tempor incididunt ut labore et dolore magna aliqua. Ut enim ad minim veniam, quis nostrud exercitation ullamco laboris nisi ut aliquip ex ea commodo consequat. Duis aute irure dolor in reprehenderit in voluptate velit esse cillum dolore eu fugiat nulla pariatur.

hPD-1
hLAG3

Lorem ipsum dolor sit amet, consectetur adipiscing elit, sed do eiusmod tempor incididunt ut labore et dolore magna aliqua. Ut enim ad minim veniam, quis nostrud exercitation ullamco laboris nisi ut aliquip ex ea commodo consequat. Duis aute irure dolor in reprehenderit in voluptate velit esse cillum dolore eu fugiat nulla pariatur.